20 April 2004
An intraabdominal desmoid tumor in a patient with familial adenomatous polyposis
Vahit Ozmen, Coskun Polat, Sezgin Yilmaz, Tolga Ozmen, Ersin SelcukCase Rep Clin Pract Rev 2004; 5(null):86-89 :: ID: 12312
Abstract
Background: Familial adenomatous polyposis is an autosomal dominant disease. It is characterized by hundreds of adenomas of the colorectal region and desmoid tumors can sometimes occur in
extracolonic manifestation of this disease.Case Report: A case of huge intraabdominal desmoid tumor invading the whole small bowel mesentery and the aorta was described. Total proctocolectomy and ileo-anal anastomosis was performed in a 42 years old woman with familial adenomatous polyposis. A huge desmoid tumor occured five years after the surgery. The tumor was 10 to 15 cm in size and multipl lymph nodes were present around it. It was originating from the mesentery of the small bowel and tightly adherent to the aorta. The frozen section of the tumor revelaed mesenchymal tumor. Estrogen receptor was positive.But the mass was considered unresectable unless the removal of the whole small intestine and the excision of the aorta were performed. vealed mesenteric fibromatosis. The patient was discharged on 4th postoperative day and then tamoxifen (20 mg daily) was prescibed. She was followed up by clinical and CT examinations. Neither clinical nor CT evidence of disease progression has been observed for eighteen months.Conclusions: This case was considered us that the progression of the desmoid tumor is affected by the hormonal influence.
Keywords: Familial adenomatous polyposis, total proctocolectomy, desmoid tumor
35
In Press
14 Mar 2024 : Case report
Management of Nontraumatic Spontaneous Renal Hemorrhage (Wünderlich Syndrome) through Robotic-Assisted Lapa...Am J Case Rep In Press; DOI: 10.12659/AJCR.942826
14 Mar 2024 : Case report
Simultaneous Occurrence of Collagen Type III Glomerulopathy and Immunoglobulin A Nephropathy: A Rare Case R...Am J Case Rep In Press; DOI: 10.12659/AJCR.942770
16 Mar 2024 : Case report
Castleman Disease Presenting in the Neck: A Report of 3 Cases and a Literature ReviewAm J Case Rep In Press; DOI: 10.12659/AJCR.943214
16 Mar 2024 : Case report
Early Diagnosis and Successful Empirical Treatment of L1-L2 Spondylodiscitis in a 21-Month-Old Girl: A Case...Am J Case Rep In Press; DOI: 10.12659/AJCR.943010
Most Viewed Current Articles
07 Mar 2024 : Case report
Neurocysticercosis Presenting as Migraine in the United StatesDOI :10.12659/AJCR.943133
Am J Case Rep 2024; 25:e943133
10 Jan 2022 : Case report
A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...DOI :10.12659/AJCR.935263
Am J Case Rep 2022; 23:e935263
19 Jul 2022 : Case report
Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19DOI :10.12659/AJCR.936128
Am J Case Rep 2022; 23:e936128
23 Feb 2022 : Case report
Penile Necrosis Associated with Local Intravenous Injection of CocaineDOI :10.12659/AJCR.935250
Am J Case Rep 2022; 23:e935250