Ameneh Yazdanfar, Kamran Kaveh
CaseRepClinPractRev 2007; 8:255-258
Background: Papillon-Lefevre syndrome (PLS) belongs to palmoplantar keratodermas(PPKs). PLS is a rare autosomal recessive disorder characterized by PPKs and keratotic plaques of the elbows and knees as well as periodontal disease with resultant premature loss of deciduous and
Case Report: Both patients are male, born and living in Malayer, Iran. There is no history of similar disease in the parents, other siblings and maternal or paternal relatives.
Conclusions: Psoriasiform lesions accompanying palmoplantar keratoderma in patients should leading the physician to examine the mouth for premature loss of teeth and to ask the patient about the family history.
Keywords: Papillon-Lefevre Disease, Keratoderma, Palmoplantar, periodontitis