06 August 2020>: Articles
Combined Emphysema and Interstitial Lung Disease as a Rare Presentation of Pulmonary Involvement in a Patient with Chronic Visceral Acid Sphingomyelinase Deficiency (Niemann-Pick Disease Type B)
Rare disease
Lucyna Opoka A* , Dorota Wyrostkiewicz A , Piotr Radwan-Rohrenschef A , Adriana Roży A , Anna Tylki-Szymańska A , Witold Tomkowski A , Monika Szturmowicz ADOI: 10.12659/AJCR.923394
Am J Case Rep 2020; 21:e923394
Figure 3. Reconstruction (3D Pulmo software) shows emphysema (areas of less than −950 HU) in red.