03 October 2023
: Case report 
A Case Report of Riboflavin Treatment and Cochlear Implants in a 4-Year-Old Girl with Progressive Hearing Loss and Delayed Speech Development: Brown-Vialetto-Van Laere Syndrome
Challenging differential diagnosis, Rare disease
Anna K. Piecuch
1ABCDEF*, Piotr H. Skarżyński 2345ADEG, Henryk Skarżyński 1AG
DOI: 10.12659/AJCR.940439
Am J Case Rep 2023; 24:e940439
Figure 2. Free-field thresholds determined by behavioral observation audiometry (BOA) and visual reinforcement audiometry (VRA) 4 months after cochlear implantation in the left ear. Right ear is open, left ear with cochlear implant. Ratio of frequency (horizontal axis) to sound intensity (vertical axis). Own elaboration. dB HL – decibels hearing level; Hz – Herz; A – threshold.