25 September 2023 : Case report
Life-Threatening Aortic Dissection during Pregnancy: A Case Report of Undiagnosed FBN1-Related Marfan Syndrome at 39 Weeks Gestation
Challenging differential diagnosis, Diagnostic / therapeutic accidents, Management of emergency care, Rare disease
Carmelina Gurrieri1ABCDEF*, Westley T. Manske1ABCDF, Carla Williams2ABDF, Joseph C. Wildenberg3ABDF, Rachel J. Keppers4BDEF, Tiziano Tallarita5BCDF, Nishant Saran5ABCDF, Andrew D. Calvin 6ABCDEFDOI: 10.12659/AJCR.940628
Am J Case Rep 2023; 24:e940628
Figure 4. Post-bypass gross photograph of the heart and ascending aorta. The aortic root was reconstructed using a valve-sparing technique. The right atrium (star) was used for central venous cannulation and later secured with a blue tourniquet. The arterial cannula has been removed and hemostasis achieved using a pledgeted purse string suture on the lateral side of the aortic graft (triangle). The right coronary artery demonstrates periarterial hematoma (arrow) from the proximal dissection, which was bypassed with a vein graft (circle). A blue vessel loop is retracting the innominate vein to better expose the innominate artery, which was reimplanted.