BACKGROUND: Foveal hypoplasia (FH) is a congenital disorder, generally associated with other conditions.

CASE REPORT: A 9-year-old boy presented with moderately decreased vision in the left eye. Fundus examination showed an absence of macular reflection and no foveal pit was seen on optical coherence tomography. Fluorescein angiography demonstrated the absence of a foveal avascular zone.

CONCLUSIONS: This is a rare case of a unilateral fovea plana associated with a visual impairment.

Keywords: Angiography, Capillaries, Fovea Centralis, Tomography, Optical Coherence, Child, Eye Diseases, Hereditary, Fluorescein Angiography, Follow-Up Studies, Nystagmus, Congenital, Rare Diseases, Risk Assessment, Vision, Low