: Case report
[In Press] Pneumatosis Cystoides Coli Presenting as Acute Abdomen in a Patient with Complicated Behcet’s Disease: A Case Report
Challenging differential diagnosis, Management of emergency care, Rare disease, Rare coexistence of disease or pathologyRachel Gefen 1ABCDEF, Brigitte Helou1B, Noam Shussman1BE, Anna Elia 2BCD, Liat Appelbaum3CD, Alon Pikarsky1AE, Jonathan Abraham Demma1ABCDEFG
Am J Case Rep In Press; DOI: :: ID: 937677
Available online: , In Press, Corrected Proof
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Behcet’s disease (BD) is defined as vasculitis involving arteries and veins of any size and affecting almost any organ system. Abdominal manifestations of BD are diverse and nonspecific. Mucosal ulcerations can be seen in the gastrointestinal tract. Extensive ulcerations, especially ileocecal lesions, can lead to perforation, strictures, fistulas, and abscesses. Pneumatosis cystoides intestinale is a rare benign condition characterized by multiple submucosal or subserosal, gas-filled cysts in the gastrointestinal tract wall. Pneumatosis cystoides coli (PCC) affects the colon, can present with a wide range of manifestations, and can mimic many different systemic diseases. We describe a case of PCC in a patient with Behcet’s disease who presented to the Emergency Department with a clinical suspicion of acute abdomen.
A 40-year-old man with complicated Behcet’s disease, treated with high-dose steroids, presented with acute abdomen and CT scan findings highly suggestive of intestinal obstruction due to ileocolic intussusception. He underwent laparoscopic right hemicolectomy. Pathology demonstrated PCC disease.
Pneumatosis cystoides coli can present with a broad range of symptoms and can be secondary to many systemic and autoimmune diseases. With radiological evidence and a high level of suspicion, unnecessary surgery can be prevented.
Keywords: Behcet Syndrome; Intussusception; Pneumatosis Cystoides Intestinalis
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