08 December 2021>: Articles
A Case Series of Adult Patients Diagnosed with IgA Vasculitis Requiring Systemic Immunosuppression
Unusual setting of medical care, Rare disease, Adverse events of drug therapy
Fenfen Cai A , Lisa Phipps A , Peter Wu A , Ming-Wei Lin A*DOI: 10.12659/AJCR.933407
Am J Case Rep 2021; 22:e933407
Table 1. IgAV cases.
Patient | Age/race/sex | Organ involvement | Biopsy results | Therapy | Outcomes |
---|---|---|---|---|---|
1 | 31/A/F | Skin-abdomen-joints- | Skin - leukocytoclastic vasculitis.Kidney – crescentic glomerulonephritis with mesangiocapillary IgA | GC, CYC, MMF | Improving proteinuria. Improving skin vasculitis |
2 | 43/I/M | Skin- | Skin – IgA vasculitis | GC, AZT | Remission |
3 | 64/T/F | Skin-abdomen- | Lung – capillaritis suggestive of vasculitis | GC, AZT – refractory, MMF – sepsis, RTX+SIR – remission | Disease remission. Hypogamma-globulinemia.Adrenal insufficiency. Infection, death |
A – Aboriginal; I – Indian; T – Turkish; M – male; F – female; GC – glucocorticoids; MMF – mycophenolate; CYC – cyclophosphamide; RTX – rituximab; SIR – sirolimus. Main organ involvement is highlighted in . |