30 April 2023 : Case report
Atypical Hemolytic Uremic Syndrome in a Pregnant Patient with a Thrombomodulin Gene Variant Treated with Plasma Exchange and Eculizumab
Challenging differential diagnosis, Unusual setting of medical care, Rare disease
Lakshmi Kannan 12ABCDEF*DOI: 10.12659/AJCR.938896
Am J Case Rep 2023; 24:e938896
Table 3. Complement-mediated TMA panel.
Complement, Total, S | 58 (30–75 U/mL) |
Complement, Alternate Path, Func, S | 92 (≥46%of norm) |
Complement C3, S | 122 (75–175 mg/dL) |
Complement C4, S | 15 (14–40 mg/dL) |
Factor B Complement Antigen, S | 38.1 (15.2–42.3 mg/dL) |
Factor H Complement Antigen, S | 27.8 (23.6–43.1mg/dL) |
C4d Complement, P | <1.4 (<9.9 mcg/mL) |
CBb Complement, P | 1.6 (<1.7 mcg/mL) |
SC5b-9 Complement, P | 149 (<251 ng/mL) |