Background: Carcinoid tumors are rare malignant neuro-endocrine tumors found mainly in the bowel and lung. They are the most common tumors of the appendix. In children, they occur more commonly in white females with a median age of 13 years.Case Report: We report here, a 14-year-old white female who presented with the clinical picture of acute appendicitis. Carcinoid tumor was diagnosed on histological examination of the removed appendix. Conclusions: Clinical presentation of carcinoid of the appendix is similar to acute appendicitis, but more commonly it is an incidental finding on appendectomy, abdominal surgery or histological examination of the surgical specimen. Localized disease has an excellent prognosis, and the tumor usually has little metastatic potential. Patients with metastatic carcinoid fare poorly. Clinical awareness and early diagnosis of carcinoid tumor of the appendix are important in preventing morbidity and mortality

Keywords: carcinoid, Appendix