Logo American Journal of Case Reports

Call: 1.631.629.4328
Mon-Fri 10 am - 2 pm EST

Contact Us

Logo American Journal of Case Reports Logo American Journal of Case Reports Logo American Journal of Case Reports

01 March 2002

Case of a neonate with Cantrell’s pentalogy complicated by
necrotizing enterocolitis

Arleta Zajączkowska-Sadlok, Kazimierz Koziołkiewicz, Piotr Korbal

Case Rep Clin Pract Rev 2002; 3(1):24-27 :: ID: 475090

Abstract

Background: Cantrell’s pentalogy is a rare congenital defect syndrome, including hernia of the umbilical cord, diaphragmatic defect, abnormalities of the sternum structure, pericardial defect and heart defect. Only 6 cases
of children with the above syndrome who survived were described before 1996. Now, advances in intensive care and new surgical techniques allow to correct more congenital defects, thus making possible further development
of the child.
Case report: The paper presents a case of a neonate, born after full-term pregnancy, operated on on the first day of life because of omphalocele, in whom detection of other anomalies contributed to the diagnosis of Cantrell’s
pentalogy with complex heart defect in the form of Fallot’s tetralogy. The post-operative course was additionally complicated by necrotizing enterocolitis, requiring exteriorization of the small intestine and long-term complete
parenteral feeding. The enterostomy was closed in the 2nd month of life. Because of retardation of psychomotor development, due probably to numerous repeated hospitalizations, the child underwent rehabilitation according to Vojta’s method, which resulted in gradual development of motor and cognitive functions. The patient required close co-operation between the parents and physicians representing many medical disciplines.
Cardiosurgical consultation led to qualification of the boy for surgical correction of heart defects which is to be performed at the age of 1 year. Then the patient is scheduled for reconstruction of the abdominal integument.
Conclusions: Therefore, Cantrell’s pentalogy seems to be one of the defect syndromes, in which survival and nearly normal development of the child is possible owing to advances in pediatric surgery, intensive care and
therapy.

Keywords: pentalogy of Cantrell, necrotizing enterocolitis, hernia of umbilical cord

Add Comment 0 Comments

19

In Press

12 Feb 2024 : Case report  Germany

Diagnostic Challenges and Imaging Considerations for Intraparotid Facial Nerve Schwannoma: A Case Report an...

Am J Case Rep In Press; DOI: 10.12659/AJCR.942870  

0:00

12 Feb 2024 : Case report  USA

Erdheim-Chester Disease Occult on Radiographs and CT but Visible on MRI and PET

Am J Case Rep In Press; DOI: 10.12659/AJCR.941169  

0:00

12 Feb 2024 : Case report  USA

Surgical Treatment of Spontaneous Superficial Temporal Artery Arteriovenous Malformation: A Case Report

Am J Case Rep In Press; DOI: 10.12659/AJCR.942839  

13 Feb 2024 : Case report  Bahrain

Warfarin Woes: A Rare Case of Hemoperitoneum with Intramural Small Bowel Hematoma

Am J Case Rep In Press; DOI: 10.12659/AJCR.943519  

Most Viewed Current Articles

10 Jan 2022 : Case report  Germany

A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...

DOI :10.12659/AJCR.935263

Am J Case Rep 2022; 23:e935263

19 Jul 2022 : Case report  Saudi Arabia

Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19

DOI :10.12659/AJCR.936128

Am J Case Rep 2022; 23:e936128

05 Mar 2022 : Case report  Brazil

Acute Limb Ischemia After Self-Injection of Crushed Morphine Tablets into the Radial Artery: Role of Infrar...

DOI :10.12659/AJCR.935336

Am J Case Rep 2022; 23:e935336

02 Apr 2022 : Case report  Saudi Arabia

Infective Endocarditis Caused by Pseudomonas luteola in a Pediatric Patient. A Case Report and Review of Li...

DOI :10.12659/AJCR.935743

Am J Case Rep 2022; 23:e935743

Your Privacy

We use cookies to ensure the functionality of our website, to personalize content and advertising, to provide social media features, and to analyze our traffic. If you allow us to do so, we also inform our social media, advertising and analysis partners about your use of our website, You can decise for yourself which categories you you want to deny or allow. Please note that based on your settings not all functionalities of the site are available. View our privacy policy.

American Journal of Case Reports eISSN: 1941-5923
American Journal of Case Reports eISSN: 1941-5923