Background: Caroli’s disease is a rare autosomal recessive condition characterized by cystic dilatation of the intrahepatic bile ducts.
Case Report: This report presents a patient who was found to have a liver lesion 10 months following an anterior resection for rectal carcinoma. This was thought to be a liver metastasis, however at surgery the lesion was found to contain stones. Histology was compatible with a diagnosis of
isolated Caroli’s disease.
Conclusions: This paper discusses this unusual presentation of what is in itself a rare condition and highlights the role of intraoperative ultrasound in the assessment of liver lesions.

Keywords: Caroli’s disease, liver metastases, intraoperative ultrasound (IOUS)