Logo American Journal of Case Reports

Call: 1.631.629.4328
Closed: National Holiday

Contact Us

Logo American Journal of Case Reports Logo American Journal of Case Reports Logo American Journal of Case Reports

25 June 2010

Acute pupillary block in an 18-month-old child with spherophakia

Almutez Gharaibeh, Mohammad Imam

Am J Case Rep 2010; 11:123-125 :: ID: 880908

Abstract

Background: Spherophakia (congenital bilateral anomaly in which the lens of the eye is small, spherical, and prone to subluxation) is a rare entity associated with systemic disorders including Weill-Marchesani syndrome, Marfan’s syndrome, Alport’s syndrome, Klinefelter’s syndrome and hyperlysinaemia. One of its well known complications is angle closure glaucoma (increased intraocular pressure secondary to physically obstructed anterior chamber angle). It is debatable whether prophylactic treatment for spherophakia is necessary or if treatment should only be performed in symptomatic patients.
Case Report: We describe an 18-month-old child with bilateral spherophakia complicated by an acute on chronic angle closure glaucoma in the right eye. To our knowledge, this is the youngest child to be reported with pupillary block secondary to anterior lens dislocation in spherophakia.
Conclusions: It seems that early intervention with lensectomy and anterior vitrectomy allows for adequate control of the intraocular pressures in patients with spherophakia.

Keywords: lensectomy, Glaucoma, spherophakia

Add Comment 0 Comments

In Press

Case report  USA

Rapid Progression of Malignant Peritoneal Mesothelioma Mimicking a Postoperative Complication in a Young Wo...

Am J Case Rep In Press; DOI: 10.12659/AJCR.942948  

0:00

Case report  Italy

Columella Reconstruction Using a Bilateral Nasolabial Flap: A Case Report

Am J Case Rep In Press; DOI: 10.12659/AJCR.943913  

0:00

Case report  USA

Successful Surgical Extraction of an Embolized Iliac Vein Stent from the Right Heart: A Case Report

Am J Case Rep In Press; DOI: 10.12659/AJCR.943620  

0:00

Case report  China (mainland)

A Forgotten Double-J Ureteric Stent as the Core of a Bladder Stone: A Case Report and Literature Review

Am J Case Rep In Press; DOI: 10.12659/AJCR.943781  

Most Viewed Current Articles

07 Mar 2024 : Case report  USA

Neurocysticercosis Presenting as Migraine in the United States

DOI :10.12659/AJCR.943133

Am J Case Rep 2024; 25:e943133

0:00

10 Jan 2022 : Case report  Germany

A Report on the First 7 Sequential Patients Treated Within the C-Reactive Protein Apheresis in COVID (CACOV...

DOI :10.12659/AJCR.935263

Am J Case Rep 2022; 23:e935263

19 Jul 2022 : Case report  Saudi Arabia

Atlantoaxial Subluxation Secondary to SARS-CoV-2 Infection: A Rare Orthopedic Complication from COVID-19

DOI :10.12659/AJCR.936128

Am J Case Rep 2022; 23:e936128

23 Feb 2022 : Case report  USA

Penile Necrosis Associated with Local Intravenous Injection of Cocaine

DOI :10.12659/AJCR.935250

Am J Case Rep 2022; 23:e935250

Your Privacy

We use cookies to ensure the functionality of our website, to personalize content and advertising, to provide social media features, and to analyze our traffic. If you allow us to do so, we also inform our social media, advertising and analysis partners about your use of our website, You can decise for yourself which categories you you want to deny or allow. Please note that based on your settings not all functionalities of the site are available. View our privacy policy.

American Journal of Case Reports eISSN: 1941-5923
American Journal of Case Reports eISSN: 1941-5923