Background: Extramammary Paget’s disease is a rare adenocarcinoma of the anogenital, axillary or umbilical regions of skin, and is derived from the apocrine glands. It is often misdiagnosed as eczema. The disease affects mainly the people over the age of 50. Biopsy is the only means that provides an accurate differential diagnosis.Case Report: This case study describes an 80 year old patient suffering from the extramammary Paget’s disease localized on the left inguinal’s skin. The diagnosis of Paget’s disease was confirmed by a histopathological examination. Conclusions: The clinical pictures of extramammary Paget’s disease still makes difficulties in everyday dermatological practice.

Keywords: extramammary Paget’s disease, histopathological examination, surgical treatment