Background: Pilomatrixoma is a solitary tumor and usually occurs in a single location. Its etiology is not clear. Surgical excision and histopathologic evaluation are necessary to identify the management of this tumor.
Case Report: We present an instance of pilomatrixoma in both of the forearms of a pediatric patient, their occurrence separated by an interval of 3 years. The tumor was superficial, well-defined, and freely mobile. The patient underwent surgical excision. The histopathological examination revealed pilomatrixoma. No recurrence was observed in 3 years of follow-up. However, 3 years after the first operation, another tumor was detected in the contralateral forearm demonstrating the same properties. The same procedure was also performed for this tumor. This patient was observed without evidence of recurrences for 3 years.
Conclusions: The management of pilomatrixoma is surgical excision, and diagnosis should be confirmed by histopathologic evaluation. It is usually seen as a single tumor; however, it is rarely multiple. Our case is of importance, since we observed pilomatrixoma in both forearms, but at different time intervals.

Keywords: Pilomatrixoma - surgery, calcifying epithelioma of Malherbe, pediatric patient